How rare is a sebaceous nevus?
How rare is a sebaceous nevus?
This is referred to as nevus sebaceus syndrome, and it is exceedingly rare. A nevus sebaceus (also known as “nevus of Jadassohn”) is an uncommon type of birthmark seen in about 0.3% of newborns. This type of birthmark is a small area of skin that has too many oil glands that grow larger than normal.
Is nevus sebaceous a genetic disorder?
LNSS is not inherited (it is sporadic). It can be caused by a somatic genetic change in any of several genes.
What does nevus sebaceous look like?
A nevus sebaceous will appear as a yellow-orange patch of skin that is hairless and smooth. It’s circumscribed, meaning that it has well-defined borders, and is likely to appear either oval or linear in shape. Typically, there will be just one patch of skin affected, and it may look like a plaque.
Can you remove nevus sebaceous?
A nevus sebaceous will not affect your child’s health, but you or your child may still want it to be taken off. If your child’s nevus sebaceous is large or becomes bothersome, it may be removed. If there are abnormal changes to the area, it may also be removed.
What is nevus sebaceous of jadassohn?
Nevus sebaceus, also called nevus sebaceus of Jadassohn or organoid nevus, is a benign hamartoma of the skin, characterized by hyperplasia of the epidermis, immature hair follicles, and sebaceous and apocrine glands.
How many people in the world have nevus sebaceous?
Approximately 0.3% of newborns are affected by nevus sebaceus, and the incidence is equal between male and female patients. The disorder affects all races and ethnicities. Usually, nevus sebaceus appears as a solitary lesion at birth.
Is a nevus sebaceous a tumor?
Nevus sebaceous is a rare benign tumor in children that usually presents with warty patches of hair loss on the scalp. The development of secondary malignant neoplasms within the nevus sebaceus is rare and occurs almost exclusively in adults.
What is the nevus sebaceus of Jadassohn?
The nevus sebaceus of Jadassohn (SNJ) is a hamartomatous disorder of the skin and its adnexa pertaining to the group of “organoid nevi,” most frequently involving the face and scalp.
What is the history of sebaceous nevus?
The condition is named for an overgrowth of sebaceous glands, a relatively uncommon hamartoma, in the area of the nevus. NSJ is first described by Josef Jadassohn in 1895. Skin growths such as benign tumors and basal cell carcinoma can arise in sebaceous nevi, usually in adulthood. Rarely, sebaceous nevi can give rise to sebaceous carcinoma.
Is nevus sebaceous cancer benign?
Though it’s technically classified as a hair follicle tumor and is associated with other conditions, a nevus sebaceous is benign. A diagnosis of nevus sebaceous is also sometimes referred to as “Jadassohn Disease II” or “organoid nevus.”
What is the incidence of malignant transformation in nevus sebaceus?
Malignant transformation within nevus sebaceus has been reported in childhood and adolescence. The incidence and lifetime risk of malignant transformation is unknown. Basal cell carcinoma (BCC) is the most common associated malignant neoplasm; the most commonly associated benign neoplasm is trichoblastoma.